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Dermatology

PREDOMINANTLY SMALL AND MEDIUM-SIZED VESSEL VASCULITIDES

Built from Dermatology, 5th Edition

The first 25 slides of PREDOMINANTLY SMALL AND MEDIUM-SIZED VESSEL VASCULITIDES
The first 25 slides, exactly as they appear. The full deck has 142 content slides.

What’s inside

11 sections · 142 slides

  1. 01

    Overview

    • Scope of this topic
    • How this topic is organised

    2 slides

  2. 02

    Background: CSVV and IgA Vasculitis

    Two baseline small-vessel entities that every disease in this topic is compared against

    • Two entities used as the yardstick
    • Cutaneous small vessel vasculitis
    • Digital infarcts in cutaneous small vessel vasculitis
    • Vesiculobullous variant of cutaneous small vessel vasculitis
    • IgA vasculitis (Henoch-Schonlein purpura)
    • Ulcerations in IgA vasculitis (Henoch-Schonlein purpura)
    • IgA vasculitis with renal involvement in an adult
    • IgA vasculitis lesions in an adult
    • Hemorrhagic Sweet syndrome mimicking vasculitis

    9 slides

  3. 03

    Acute Hemorrhagic Edema of Infancy

    A dramatic-looking but benign small-vessel vasculitis of infants and toddlers

    • What is acute hemorrhagic edema of infancy
    • Epidemiology of acute hemorrhagic edema of infancy
    • Pathogenesis of acute hemorrhagic edema of infancy
    • Triggers in acute hemorrhagic edema of infancy
    • Triggers in acute hemorrhagic edema of infancy
    • Clinical features of AHEI: the rash
    • What the rash of AHEI looks like
    • Acute hemorrhagic edema of infancy: thigh and sole lesions
    • Clinical course of acute hemorrhagic edema of infancy
    • Pathology of acute hemorrhagic edema of infancy
    • Differential diagnosis of acute hemorrhagic edema of infancy
    • Treatment of acute hemorrhagic edema of infancy

    12 slides

  4. 04

    Urticarial Vasculitis

    Hive-like lesions that are actually true blood vessel inflammation

    • What is urticarial vasculitis
    • Epidemiology of urticarial vasculitis
    • How urticarial vasculitis develops
    • Conditions associated with urticarial vasculitis
    • Conditions associated with urticarial vasculitis
    • Skin findings in urticarial vasculitis
    • What urticarial vasculitis looks like
    • Hypocomplementemic urticarial vasculitis syndrome (HUVS)
    • Organ involvement in urticarial vasculitis and HUVS
    • Laboratory findings in urticarial vasculitis
    • Pathology of urticarial vasculitis
    • Differential diagnosis of urticarial vasculitis
    • Treatment of urticarial vasculitis

    13 slides

  5. 05

    Erythema Elevatum Diutinum

    A rare, long-lasting small-vessel vasculitis that scars into fibrous nodules over joints

    • What is erythema elevatum diutinum
    • Epidemiology of erythema elevatum diutinum
    • How erythema elevatum diutinum develops
    • Conditions associated with erythema elevatum diutinum
    • Clinical features of erythema elevatum diutinum
    • What EED lesions look like
    • Course and eye disease in erythema elevatum diutinum
    • Erythema elevatum diutinum: histopathologic features
    • Differential diagnosis of erythema elevatum diutinum
    • Treatment of erythema elevatum diutinum

    10 slides

  6. 06

    Granuloma Faciale

    A chronic, usually solitary, facial small-vessel vasculitis

    • What is granuloma faciale
    • Epidemiology and pathogenesis of granuloma faciale
    • Clinical features of granuloma faciale
    • What granuloma faciale looks like
    • Pathology of granuloma faciale
    • Granuloma faciale: histopathologic features
    • Differential diagnosis of granuloma faciale
    • Treatment of granuloma faciale

    8 slides

  7. 07

    Cryoglobulinemic Vasculitis

    A mixed small- and medium-vessel vasculitis driven, in most cases, by hepatitis C infection

    • What are cryoglobulins
    • Classification of cryoglobulins
    • Classification of cryoglobulins: I
    • Classification of cryoglobulins: II / III
    • Epidemiology of cryoglobulinemic vasculitis
    • How cryoglobulinemic vasculitis develops
    • Skin and organ findings in cryoglobulinemic vasculitis
    • What cryoglobulinemic vasculitis looks like
    • Laboratory testing in cryoglobulinemic vasculitis
    • Cutaneous vasculitis due to mixed cryoglobulinemia
    • Pathology and differential diagnosis of cryoglobulinemic vasculitis
    • Treatment of cryoglobulinemic vasculitis

    12 slides

  8. 08

    ANCA-Associated Vasculitides

    Three overlapping small-to-medium vessel vasculitides defined by anti-neutrophil cytoplasmic antibodies

    • What are the ANCA-associated vasculitides
    • The two ANCA staining patterns
    • Comparing GPA, MPA, and EGPA
    • ANCA-associated vasculitides: Granulomatosis with polyangiitis (GPA; formerly Wegener granulomatosis) - most often c-ANCA/anti-PR3 antibody
    • ANCA-associated vasculitides: Microscopic polyangiitis (MPA) - most often p-ANCA/anti-MPO antibody
    • ANCA-associated vasculitides: Eosinophilic granulomatosis with polyangiitis (EGPA; formerly Churg-Strauss syndrome) - most often ANCA-negative or p-ANCA/anti-MPO antibody
    • Epidemiology and mechanism of the ANCA-associated vasculitides
    • What is granulomatosis with polyangiitis
    • Epidemiology and pathogenesis of granulomatosis with polyangiitis
    • Skin and mucosal findings in granulomatosis with polyangiitis
    • What granulomatosis with polyangiitis looks like
    • Airway and lung findings in granulomatosis with polyangiitis
    • Kidney and other organ findings in granulomatosis with polyangiitis
    • Additional testing for suspected ANCA-associated vasculitis
    • Additional diagnostic testing for suspected ANCA-associated vasculitis
    • Leg ulcer in granulomatosis with polyangiitis
    • Churg-Strauss nodules of the elbow in granulomatosis with polyangiitis
    • Pathology of granulomatosis with polyangiitis
    • Distinguishing GPA from its differential diagnosis
    • Key disorders in the differential diagnosis of ANCA-associated vasculitis
    • Key disorders in the differential diagnosis of ANCA-associated vasculitis (continued)
    • Treatment of granulomatosis with polyangiitis: induction
    • Treatment of granulomatosis with polyangiitis: maintenance
    • What is microscopic polyangiitis
    • Epidemiology and skin findings in microscopic polyangiitis
    • What microscopic polyangiitis looks like
    • Organ disease, pathology, and treatment of microscopic polyangiitis
    • What is eosinophilic granulomatosis with polyangiitis
    • Epidemiology of eosinophilic granulomatosis with polyangiitis
    • How eosinophilic granulomatosis with polyangiitis develops
    • The three phases of eosinophilic granulomatosis with polyangiitis
    • Skin and organ findings in eosinophilic granulomatosis with polyangiitis
    • What eosinophilic granulomatosis with polyangiitis looks like
    • Labs, pathology, and differential diagnosis of EGPA
    • Treatment of eosinophilic granulomatosis with polyangiitis

    35 slides

  9. 09

    Polyarteritis Nodosa

    A multi-system vasculitis of predominantly medium-sized arteries, with a milder skin-limited form

    • What is polyarteritis nodosa
    • Epidemiology of polyarteritis nodosa
    • How polyarteritis nodosa develops
    • Clinical features of systemic (classic) polyarteritis nodosa
    • Skin findings in systemic polyarteritis nodosa
    • What polyarteritis nodosa looks like
    • Cutaneous polyarteritis nodosa
    • Laboratory and imaging findings in polyarteritis nodosa
    • Cutaneous polyarteritis nodosa: histopathologic features
    • Differential diagnosis of polyarteritis nodosa
    • Lymphocytic thrombophilic arteritis, a PAN look-alike
    • Treatment of polyarteritis nodosa

    12 slides

  10. 10

    Giant Cell (Temporal) Arteritis

    A large-vessel vasculitis that occasionally reaches the skin of the scalp and tongue

    • Temporal arteritis and the skin
    • Temporal arteritis
    • Diagnosis and treatment of temporal arteritis

    3 slides

  11. 11

    Diagnostic Approach to Suspected Vasculitis

    Correlating the clinical picture with pathology, screening for systemic disease, and matching treatment to severity

    • Approach to a patient with suspected vasculitis
    • Physical examination in suspected vasculitis
    • Morphologic approach to suspected cutaneous vasculitis
    • Skin biopsy in suspected vasculitis
    • Laboratory evaluation of suspected vasculitis
    • Approach to suspected cutaneous small vessel vasculitis
    • Principles of vasculitis treatment
    • Summary: telling these vasculitides apart
    • Key take-home points
    • References
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    • Dermatology, 5th Edition (2-Volume Set)

    26 slides