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Dermatology

Other Lymphoproliferative and Myeloproliferative Diseases

Built from Dermatology, 5th Edition

The first 25 slides of Other Lymphoproliferative and Myeloproliferative Diseases
The first 25 slides, exactly as they appear. The full deck has 101 content slides.

What’s inside

4 sections · 101 slides

  1. 01

    Overview

    • What this topic covers
    • Why the skin gets involved in blood disorders

    2 slides

  2. 02

    Benign Lymphocytic Infiltrates

    Reactive immune reactions in the skin that can closely resemble cutaneous lymphoma

    • Lymphocytic infiltrate of Jessner (LIJ)
    • Lymphocytic infiltrate of Jessner: cause
    • Lymphocytic infiltrate of Jessner: clinical appearance
    • Lymphocytic infiltrate of Jessner: arciform plaques on the back
    • Lymphocytic infiltrate of Jessner: confluent papules on the cheek
    • Lymphocytic infiltrate of Jessner: annular plaques of the central back
    • Lymphocytic infiltrate of Jessner: pathology
    • Distinguishing lymphocytic infiltrate of Jessner from its mimics
    • Lymphocytic infiltrate of Jessner: telling it apart from mimics
    • Lymphocytic infiltrate of Jessner: treatment
    • Cutaneous lymphoid hyperplasia (pseudolymphoma)
    • Cutaneous lymphoid hyperplasia: who gets it, and why
    • Medications associated with cutaneous lymphoid hyperplasia (pseudolymphoma)
    • Medications associated with cutaneous lymphoid hyperplasia (pseudolymphoma) (continued)
    • Cutaneous lymphoid hyperplasia: clinical appearance
    • Cutaneous lymphoid hyperplasia: ear and leech-bite presentations
    • Cutaneous lymphoid hyperplasia: further Borrelia- and leech-associated presentations
    • Miliarial-type perifollicular B cell pseudolymphoma
    • Cutaneous lymphoid hyperplasia: B cell-predominant pathology
    • Microscopic differences between cutaneous lymphoid hyperplasia (pseudolymphoma) and primary cutaneous follicle center lymphoma
    • Microscopic differences between cutaneous lymphoid hyperplasia (pseudolymphoma) and primary cutaneous follicle center lymphoma (continued)
    • Cutaneous lymphoid hyperplasia: T cell and CD30+ patterns
    • Acral pseudolymphomatous angiokeratoma of children (APACHE)
    • Kikuchi-Fujimoto disease
    • Pseudolymphomatous folliculitis
    • Cutaneous and systemic plasmacytosis
    • Intralymphatic histiocytosis
    • Entities that mimic cutaneous lymphoma: more common
    • Entities that mimic cutaneous lymphoma: uncommon
    • Entities that mimic cutaneous lymphoma: rare
    • Cutaneous lymphoid hyperplasia: treatment

    31 slides

  3. 03

    Cutaneous Extramedullary Hematopoiesis

    Blood cells forming in the skin instead of the bone marrow - from the newborn 'blueberry muffin baby' to adult marrow disease

    • Cutaneous extramedullary hematopoiesis (CEMH)
    • Cutaneous extramedullary hematopoiesis: cause
    • Cutaneous extramedullary hematopoiesis: the "blueberry muffin baby"
    • Blueberry muffin baby: a second example of congenital rubella
    • Differential diagnosis of “blueberry muffin baby”
    • Cutaneous extramedullary hematopoiesis: pathology and diagnosis
    • Retiform purpura in advanced myelofibrosis
    • Cutaneous extramedullary hematopoiesis: treatment

    8 slides

  4. 04

    Malignant Hematopoietic Infiltrates

    True leukemia and lymphoma cells living in the skin, from common leukemia cutis to four rarer, aggressive entities

    • Five malignant infiltrates covered in this section
    • Leukemia cutis
    • Leukemia cutis: which leukemia, which patient
    • How a chromosome swap drives one type of leukemia
    • Leukemia cutis: other prognostic gene changes
    • Relationship between specific molecular abnormalities and prognosis in chronic lymphocytic leukemia
    • Leukemia cutis: clinical appearance
    • Leukemia cutis in hairy cell leukemia
    • Leukemia cutis: less typical presentations
    • Inflammatory” disorders associated with leukemias and myelodysplastic syndromes 18 – 21
    • Inflammatory” disorders associated with leukemias and myelodysplastic syndromes 18 – 21 (continued)
    • Inflammatory” disorders associated with leukemias and myelodysplastic syndromes 18 – 21 (continued)
    • Leukemia cutis: the timing puzzle
    • Leukemia cutis: ALL characteristics
    • Leukemia cutis: CLL characteristics
    • Leukemia cutis: AML characteristics
    • Leukemia cutis: CML characteristics
    • Leukemia cutis: pathology by leukemia type
    • Chronic lymphocytic leukemia (CLL): pathology
    • Leukemia cutis: differential diagnosis and treatment
    • Cutaneous Hodgkin lymphoma
    • Cutaneous Hodgkin lymphoma: who gets it, and why
    • Cutaneous Hodgkin lymphoma: clinical features
    • Cutaneous Hodgkin lymphoma: papulonodules with a larger hip tumor
    • Cutaneous Hodgkin lymphoma: plaque with central clearing
    • Cutaneous Hodgkin lymphoma: paraneoplastic skin signs
    • Cutaneous Hodgkin lymphoma: pathology
    • Cutaneous Hodgkin lymphoma: pathology showing a Reed-Sternberg cell
    • Cutaneous Hodgkin lymphoma: differential diagnosis and treatment
    • Blastic plasmacytoid dendritic cell neoplasm (BPDCN)
    • BPDCN: cause and disease course
    • BPDCN: clinical appearance
    • BPDCN: two nodules on the cheek
    • BPDCN: pathology
    • BPDCN: immunophenotype and molecular findings
    • BPDCN: differential diagnosis and treatment
    • Angioimmunoblastic T cell lymphoma (AITL)
    • AITL: cause
    • AITL: skin findings
    • AITL: associated abnormalities and outlook
    • AITL: five patterns seen in skin biopsies
    • AITL: immunophenotype and molecular findings
    • AITL: differential diagnosis and treatment
    • Lymphomatoid granulomatosis (LG)
    • Lymphomatoid granulomatosis: cause and lung symptoms
    • Lymphomatoid granulomatosis: skin involvement
    • Lymphomatoid granulomatosis: three histologic grades
    • Lymphomatoid granulomatosis: more pathology detail
    • Lymphomatoid granulomatosis: differential diagnosis and treatment
    • Reactive vs. malignant: how to tell them apart
    • Key takeaways
    • References
    • References (continued)
    • References (continued)
    • References (continued)
    • References (continued)
    • References (continued)
    • References (continued)
    • References (continued)
    • Dermatology, 5th Edition (2-Volume Set)

    60 slides