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Dermatology

Deposition Diseases

Built from Dermatology, 5th Edition

The first 25 slides of Deposition Diseases
The first 25 slides, exactly as they appear. The full deck has 75 content slides.

What’s inside

6 sections · 75 slides

  1. 01

    Overview

    • What is a cutaneous deposition disease
    • Five deposition diseases covered here
    • Telling deposition diseases apart on biopsy
    • Disorders with dermal deposits - histologic features
    • Disorders with dermal deposits - histologic features (continued)
    • Disorders with dermal deposits - histologic features (continued)

    6 slides

  2. 02

    Gout

    Urate crystal arthropathy - the most common crystal-induced arthritis

    • What gout is
    • Epidemiology of gout
    • How uric acid builds up: overproduction vs under-excretion
    • Classification of hyperuricemia
    • From crystals to inflammation
    • Four clinical stages of gout
    • Acute gouty arthritis
    • Chronic tophaceous gout
    • Tophaceous gout of a digit
    • Tophaceous gout of the tragus
    • Gout pathology on biopsy
    • Tophaceous gout - histopathologic features
    • Staining the crystals
    • Tophaceous gout - localized to extensive
    • Tophaceous gout involving the ear
    • Tophaceous gout - amorphous dermal deposits
    • Tophaceous gout - needle-like clefts on higher magnification
    • Differential diagnosis of gout
    • Treating an acute gout attack
    • Lowering uric acid long-term
    • Allopurinol and febuxostat side effects
    • Other gout treatments

    22 slides

  3. 03

    Pseudogout

    Calcium pyrophosphate dihydrate crystal disease

    • What pseudogout is
    • Pseudogout mechanism and symptoms
    • Pseudogout - histopathologic features
    • Gout vs pseudogout at a glance
    • Treating pseudogout

    5 slides

  4. 04

    Lipoid Proteinosis

    Hyalinosis cutis et mucosae - Urbach-Wiethe disease

    • What lipoid proteinosis is
    • Who gets lipoid proteinosis
    • ECM1: the gene behind lipoid proteinosis
    • Three ECM1 protein isoforms
    • Lipoid proteinosis: stage 1 (infancy)
    • Lipoid proteinosis: stage 2 (skin thickening)
    • Lipoid proteinosis - clinical features
    • Beyond the skin: mouth, teeth, and brain
    • Lipoid proteinosis on biopsy
    • Lipoid proteinosis - biopsy findings
    • Differential diagnosis of lipoid proteinosis
    • Treating lipoid proteinosis

    12 slides

  5. 05

    Colloid Milium

    Colloid degeneration of sun-damaged skin

    • What colloid milium is
    • Who gets colloid milium and why
    • What colloid milium looks like
    • Juvenile and adult colloid milium
    • Adult colloid milium on biopsy
    • Adult colloid milium - biopsy findings
    • Adult colloid milium - additional biopsy view
    • Juvenile, pigmented, and nodular variants
    • Differential diagnosis of colloid milium
    • Treating colloid milium

    10 slides

  6. 06

    Mucopolysaccharidoses

    Inherited lysosomal enzyme deficiencies that let sugar chains build up

    • What the mucopolysaccharidoses are
    • Skin signs of MPS, and Hunter syndrome pebbling
    • Dermal melanocytosis and hypertrichosis in Hunter syndrome
    • Diagnosing MPS
    • MPS findings on biopsy
    • The mucopolysaccharidoses at a glance
    • The mucopolysaccharidoses - enzyme, storage, and inheritance
    • The mucopolysaccharidoses - enzyme, storage, and inheritance (continued)
    • The mucopolysaccharidoses - enzyme, storage, and inheritance (continued)
    • The mucopolysaccharidoses - organ involvement
    • The mucopolysaccharidoses - organ involvement (continued)
    • The mucopolysaccharidoses - organ involvement (continued)
    • Treating the mucopolysaccharidoses
    • Stem cell transplant and future therapies
    • Key takeaways
    • References
    • References (continued)
    • References (continued)
    • References (continued)
    • Dermatology, 5th Edition (2-Volume Set)

    20 slides